Contributor: Gordon K. Klintworth
Nevus flammeus (port-wine stain, port-wine spot, capillary hemangioma) is a congenital diffuse poorly demarcated nevus characterized by cutaneous capillary hemangiomas [hemangioma - capillary] of the face, scalp and neck that range in color from pink to dark bluish red. It is cardinal feature of Sturge-Weber syndrome. A capillary hemangioma is benign vascular tumor composed of capillaries. It is usually not encapsulated and is composed of numerous capillaries and developing thin-walled vessels lined by endothelial cells. Nevus flammeus frequently involve the eyelid and occur in childhood.