Contributor: Gordon K. Klintworth
Klippel-Trénaunay-Weber syndrome (Klippel-Trénaunay syndrome) is a rare syndrome with a persistent nevus flammeus related to Sturge-Weber syndrome that usually affects one extremity. The affected limb is characterized by hypertrophy of the bone and soft tissue and has large hemangiomas of the skin and varices. A web site provides information for patients on the Klippel-Trénaunay syndrome (http://www.sturge-weber.com).